Atlas Two · Pathogen Atlas · 05-prions

Prion Protein

Prion protein: PrPC (normal, α-helical) vs. PrPSc (pathological, β-sheet-rich). PrPSc propagates by templating PrPC misfolding; resists protease, heat, formalin. Causes CJD, kuru, FFI, GSS. 100% fatality. No nucleic acid genome; pure protein pathogen.

Also known as: PrP, prion, PrPSc, PrPC, scrapie prion, misfolded prion

05-prionsClass
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2026-06-05Last Reviewed
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prion-protein

Prion Protein

Prion protein: PrPC (normal, α-helical) vs. PrPSc (pathological, β-sheet-rich). PrPSc propagates by templating PrPC misfolding; resists protease, heat, formalin. Causes CJD, kuru, FFI, GSS. 100% fatality. No nucleic acid genome; pure protein pathogen.