Atlas One · Host Biology · Scale 07 — System

Hereditary Angioedema

Hereditary angioedema (HAE) is recurrent bradykinin-mediated swelling from C1-INH deficiency; laryngeal HAE causes asphyxiation. Icatibant (B2R antagonist) and C1-INH concentrate for acute attacks; berotralstat and lanadelumab for long-term prophylaxis.

Also known as: HAE, hereditary angioedema, HAE type I, HAE type II, HAE type III, C1 inhibitor deficiency, SERPING1 deficiency, bradykinin angioedema, Quincke's edema

Scale 07 — SystemScale
draftStatus
2026-06-07Last Reviewed
This is an auto-generated stub page built from atlas entry frontmatter. A richer hand-crafted page is planned. See the atlas source for the full entry including detailed body sections.
hereditary-angioedema

Hereditary Angioedema

Hereditary angioedema (HAE) is recurrent bradykinin-mediated swelling from C1-INH deficiency; laryngeal HAE causes asphyxiation. Icatibant (B2R antagonist) and C1-INH concentrate for acute attacks; berotralstat and lanadelumab for long-term prophylaxis.

Entry Metadata

FieldValue
IDhereditary-angioedema
NameHereditary Angioedema
Statusdraft
Last reviewed2026-06-07
Atlas01-human
Scale07-system

Cross-Atlas Connections

connects-toC1 Esterase Inhibitor connects-toComplement C3 connects-toBradykinin connects-toAngiotensin Ii connects-toThrombin connects-toEndothelial Cell connects-toSkin connects-toEstrogen connects-toImmune System connects-toMast Cell connects-toLiver connects-toDigestive System connects-toRespiratory System connects-toHypertension connects-toComplement C5 connects-toAsthma connects-toAtopic Dermatitis connects-toSmall Intestine connects-toNitric Oxide connects-toSystemic Lupus Erythematosus connects-toHistamine connects-toReproductive System connects-toSmooth Muscle Cell connects-toTestosterone connects-toPlasma Cell connects-toLymphatic System connects-toVegf connects-toCalcium connects-toCortisol connects-toOxygen connects-toLarge Intestine connects-toKidney connects-toLung connects-toHepatocyte connects-toPhoton connects-toElectron connects-toEye connects-toBrain connects-toStomach connects-toAntibody connects-toAlbumin connects-toPancreas connects-toNeuron connects-toMajor Depressive Disorder connects-toHelicobacter Pylori connects-toCll connects-toB Cell connects-toProstaglandins connects-toNeutrophil connects-toPanic Disorder connects-toIntestinal Epithelium connects-toAce2 connects-toGeneralized Anxiety Disorder connects-toHcc connects-toVenous Thromboembolism connects-toType 2 Diabetes connects-toAtherosclerosis connects-toPtsd connects-toSepsis connects-toIntegumentary System connects-toEndocrine System connects-toCardiovascular System connects-toNervous System connects-toRenal System connects-toMusculoskeletal System connects-toAce Inhibitors connects-toHelicobacter Pylori connects-toMultiple Myeloma connects-toTargeted Therapy connects-toArbs connects-toCorticosteroids connects-toCovid 19 Disease connects-toCancer Chemotherapy connects-toAspirin connects-toHereditary Pancreatitis connects-toDlbcl connects-toArterial Wall connects-toHepatic Lobule connects-toWaldenstrom Macroglobulinemia connects-toGerminal Center connects-toFollicular Lymphoma connects-toMantle Cell Lymphoma connects-toSpleen connects-toAngiopoietin connects-toFibrinogen connects-toVon Willebrand Factor connects-toPlatelet connects-toIge connects-toGlucocorticoid Receptor connects-toAntithrombin connects-toAdrenomedullin connects-toRenin connects-toFcrn connects-toC5Ar1 connects-toEndothelin 1 connects-toNf Kb connects-toIl 6 connects-toTnf Alpha connects-toSubstance P connects-toCgrp connects-toProtein C connects-toAkt connects-toErk1 2 connects-toNlrp3 Inflammasome connects-toPik3Ca connects-toGalectin 3 connects-toStat3 connects-toJak1 2 connects-toHif 1Alpha connects-toFoxo connects-toGsk 3B connects-toS100A8 A9 connects-toMtor connects-toSrc Kinase connects-toStat1 connects-toNfe2L2 connects-toAmpk connects-toAutophagy connects-toDnmt3A connects-toCxcl12 connects-toAdenosine connects-toIl 1B connects-toProgesterone connects-toIl 33 connects-toIl 17A connects-toImmunoglobulin G connects-toMhc Class Ii connects-toIl 2 connects-toAldosterone connects-toIl 10 connects-toT Helper Cell connects-toZinc connects-toIl 4 connects-toIl 13 connects-toBaff connects-toCd20 connects-toType I Interferon connects-toLeptin connects-toAdiponectin connects-toResistin connects-toNatural Killer Cell connects-toIfn Gamma connects-toIl 12 connects-toIl 5 connects-toIl 23 connects-toDendritic Cell connects-toFactor H connects-toMacrophage connects-toT Cytotoxic Cell connects-toRegulatory T Cell connects-toOsteopontin connects-toTransferrin connects-toTslp connects-toErythropoietin connects-toPeriostin connects-toMelatonin connects-toProlactin connects-toOxytocin connects-toSerotonin connects-toVasopressin connects-toSelenium connects-toIodine connects-toSodium connects-toMagnesium connects-toCopper connects-toPhosphorus connects-toPotassium connects-toIron connects-toChloride connects-toCarbon connects-toNitrogen connects-toSulfur connects-toHydrogen connects-toPd 1 connects-toGlp 1 connects-toWnt Beta Catenin connects-toRankl connects-toSmad4 connects-toFibronectin connects-toNotch connects-toIgf 1 connects-toActivin A connects-toTgf Beta connects-toCalcitonin connects-toInsulin Receptor connects-toAndrogen Receptor connects-toNorepinephrine connects-toBdnf connects-toFgfr connects-toEpinephrine connects-toMyostatin connects-toGhrelin connects-toGlucagon