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hereditary-angioedema
Hereditary Angioedema
Hereditary angioedema (HAE) is recurrent bradykinin-mediated swelling from C1-INH deficiency; laryngeal HAE causes asphyxiation. Icatibant (B2R antagonist) and C1-INH concentrate for acute attacks; berotralstat and lanadelumab for long-term prophylaxis.
Entry Metadata
| Field | Value |
|---|---|
| ID | hereditary-angioedema |
| Name | Hereditary Angioedema |
| Status | draft |
| Last reviewed | 2026-06-07 |
| Atlas | 01-human |
| Scale | 07-system |
Cross-Atlas Connections
connects-toC1 Esterase Inhibitor
connects-toComplement C3
connects-toBradykinin
connects-toAngiotensin Ii
connects-toThrombin
connects-toEndothelial Cell
connects-toSkin
connects-toEstrogen
connects-toImmune System
connects-toMast Cell
connects-toLiver
connects-toDigestive System
connects-toRespiratory System
connects-toHypertension
connects-toComplement C5
connects-toAsthma
connects-toAtopic Dermatitis
connects-toSmall Intestine
connects-toNitric Oxide
connects-toSystemic Lupus Erythematosus
connects-toHistamine
connects-toReproductive System
connects-toSmooth Muscle Cell
connects-toTestosterone
connects-toPlasma Cell
connects-toLymphatic System
connects-toVegf
connects-toCalcium
connects-toCortisol
connects-toOxygen
connects-toLarge Intestine
connects-toKidney
connects-toLung
connects-toHepatocyte
connects-toPhoton
connects-toElectron
connects-toEye
connects-toBrain
connects-toStomach
connects-toAntibody
connects-toAlbumin
connects-toPancreas
connects-toNeuron
connects-toMajor Depressive Disorder
connects-toHelicobacter Pylori
connects-toCll
connects-toB Cell
connects-toProstaglandins
connects-toNeutrophil
connects-toPanic Disorder
connects-toIntestinal Epithelium
connects-toAce2
connects-toGeneralized Anxiety Disorder
connects-toHcc
connects-toVenous Thromboembolism
connects-toType 2 Diabetes
connects-toAtherosclerosis
connects-toPtsd
connects-toSepsis
connects-toIntegumentary System
connects-toEndocrine System
connects-toCardiovascular System
connects-toNervous System
connects-toRenal System
connects-toMusculoskeletal System
connects-toAce Inhibitors
connects-toHelicobacter Pylori
connects-toMultiple Myeloma
connects-toTargeted Therapy
connects-toArbs
connects-toCorticosteroids
connects-toCovid 19 Disease
connects-toCancer Chemotherapy
connects-toAspirin
connects-toHereditary Pancreatitis
connects-toDlbcl
connects-toArterial Wall
connects-toHepatic Lobule
connects-toWaldenstrom Macroglobulinemia
connects-toGerminal Center
connects-toFollicular Lymphoma
connects-toMantle Cell Lymphoma
connects-toSpleen
connects-toAngiopoietin
connects-toFibrinogen
connects-toVon Willebrand Factor
connects-toPlatelet
connects-toIge
connects-toGlucocorticoid Receptor
connects-toAntithrombin
connects-toAdrenomedullin
connects-toRenin
connects-toFcrn
connects-toC5Ar1
connects-toEndothelin 1
connects-toNf Kb
connects-toIl 6
connects-toTnf Alpha
connects-toSubstance P
connects-toCgrp
connects-toProtein C
connects-toAkt
connects-toErk1 2
connects-toNlrp3 Inflammasome
connects-toPik3Ca
connects-toGalectin 3
connects-toStat3
connects-toJak1 2
connects-toHif 1Alpha
connects-toFoxo
connects-toGsk 3B
connects-toS100A8 A9
connects-toMtor
connects-toSrc Kinase
connects-toStat1
connects-toNfe2L2
connects-toAmpk
connects-toAutophagy
connects-toDnmt3A
connects-toCxcl12
connects-toAdenosine
connects-toIl 1B
connects-toProgesterone
connects-toIl 33
connects-toIl 17A
connects-toImmunoglobulin G
connects-toMhc Class Ii
connects-toIl 2
connects-toAldosterone
connects-toIl 10
connects-toT Helper Cell
connects-toZinc
connects-toIl 4
connects-toIl 13
connects-toBaff
connects-toCd20
connects-toType I Interferon
connects-toLeptin
connects-toAdiponectin
connects-toResistin
connects-toNatural Killer Cell
connects-toIfn Gamma
connects-toIl 12
connects-toIl 5
connects-toIl 23
connects-toDendritic Cell
connects-toFactor H
connects-toMacrophage
connects-toT Cytotoxic Cell
connects-toRegulatory T Cell
connects-toOsteopontin
connects-toTransferrin
connects-toTslp
connects-toErythropoietin
connects-toPeriostin
connects-toMelatonin
connects-toProlactin
connects-toOxytocin
connects-toSerotonin
connects-toVasopressin
connects-toSelenium
connects-toIodine
connects-toSodium
connects-toMagnesium
connects-toCopper
connects-toPhosphorus
connects-toPotassium
connects-toIron
connects-toChloride
connects-toCarbon
connects-toNitrogen
connects-toSulfur
connects-toHydrogen
connects-toPd 1
connects-toGlp 1
connects-toWnt Beta Catenin
connects-toRankl
connects-toSmad4
connects-toFibronectin
connects-toNotch
connects-toIgf 1
connects-toActivin A
connects-toTgf Beta
connects-toCalcitonin
connects-toInsulin Receptor
connects-toAndrogen Receptor
connects-toNorepinephrine
connects-toBdnf
connects-toFgfr
connects-toEpinephrine
connects-toMyostatin
connects-toGhrelin
connects-toGlucagon
Sources
- Cicardi M, Banerji A, Bracho F, et al. Icatibant, a new bradykinin-receptor antagonist, in hereditary angioedema. N Engl J Med. 2010;363(6):532-541. · PubMed 20818873
- Banerji A, Riedl MA, Bernstein JA, et al. Effect of lanadelumab compared with placebo on prevention of hereditary angioedema attacks: a randomized clinical trial. JAMA. 2018;320(20):2108-2121. · PubMed 30480729
- Zuraw BL, Busse PJ, White M, et al. Berotralstat (BCX7353) for the prevention of hereditary angioedema. N Engl J Med. 2021;384(23):2186-2195. · PubMed 34077648