Atlas One · Host Biology · Scale 07 — System

Waldenström Macroglobulinemia

Waldenström macroglobulinemia is lymphoplasmacytic lymphoma producing IgM monoclonal protein; MYD88 L265P in ~90% drives NF-κB and JAK-STAT3. Hyperviscosity, neuropathy, and cryoglobulinemia are hallmarks; ibrutinib and zanubrutinib are approved for MYD88 L265P WM.

Also known as: Waldenström macroglobulinemia, WM, lymphoplasmacytic lymphoma, LPL, IgM monoclonal protein, IgM paraprotein, hyperviscosity syndrome, MYD88 L265P WM

Scale 07 — SystemScale
draftStatus
2026-06-06Last Reviewed
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waldenstrom-macroglobulinemia

Waldenström Macroglobulinemia

Waldenström macroglobulinemia is lymphoplasmacytic lymphoma producing IgM monoclonal protein; MYD88 L265P in ~90% drives NF-κB and JAK-STAT3. Hyperviscosity, neuropathy, and cryoglobulinemia are hallmarks; ibrutinib and zanubrutinib are approved for MYD88 L265P WM.