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immune-thrombocytopenia
Immune Thrombocytopenia
Immune thrombocytopenia (ITP): anti-platelet IgG (anti-GPIIb/IIIa) → FcγR-mediated splenic destruction + CD8+ T-cell lysis; platelet <100×10⁹/L. Corticosteroids/IVIG first-line; romiplostim, eltrombopag (TPO-RAs); efgartigimod (FcRn inhibitor; FDA Jun 2023).
Entry Metadata
| Field | Value |
|---|---|
| ID | immune-thrombocytopenia |
| Name | Immune Thrombocytopenia |
| Status | draft |
| Last reviewed | 2026-06-07 |
| Atlas | 01-human |
| Scale | 07-system |
Cross-Atlas Connections
modulated-byThrombopoietin
connects-toFcrn
modulated-byImmunoglobulin G
connects-toPlatelet
connects-toSpleen
connects-toMacrophage
connects-toHelicobacter Pylori
connects-toIga Nephropathy
connects-toB Cell
connects-toSystemic Lupus Erythematosus
connects-toHepatitis C
connects-toCll
connects-toBone Marrow
connects-toThrombotic Thrombocytopenic Purpura
connects-toDisseminated Intravascular Coagulation
connects-toAntiphospholipid Syndrome
connects-toPlasma Cell
connects-toHiv Aids
connects-toT Helper Cell
connects-toImmune System
connects-toNervous System
connects-toEpstein Barr Virus
connects-toT Cytotoxic Cell
connects-toMeasles
connects-toPlacenta
connects-toCortisol
connects-toRegulatory T Cell
connects-toLiver
connects-toCd20
connects-toBrain
connects-toDendritic Cell
connects-toIron
connects-toSkin
connects-toComplement C3
connects-toPhoton
connects-toLarge Intestine
connects-toGerminal Center
connects-toElectron
connects-toEye
connects-toKidney
connects-toAntibody
connects-toErythrocyte
connects-toVitamin D
connects-toReproductive System
connects-toBtk
connects-toVaricella Zoster Virus
connects-toAplastic Anemia
connects-toNatural Killer Cell
connects-toVon Willebrand Factor
connects-toComplement C5
connects-toVenous Thromboembolism
connects-toCovid 19 Disease
connects-toStat3
connects-toNf Kb
connects-toSepsis
connects-toHiv
connects-toPneumocystis Jirovecii
connects-toMajor Depressive Disorder
connects-toStroke
connects-toAspergillus Fumigatus
connects-toOsteoporosis
connects-toIntegumentary System
connects-toDigestive System
connects-toGeneralized Anxiety Disorder
connects-toLymphatic System
connects-toEndocrine System
connects-toMusculoskeletal System
connects-toCorticosteroids
connects-toCardiovascular System
connects-toRenal System
connects-toHepatitis C Virus
connects-toHeparin Induced Thrombocytopenia
connects-toCancer Chemotherapy
connects-toDexamethasone
connects-toHodgkin Lymphoma
connects-toRheumatoid Arthritis
connects-toMds
connects-toFollicular Lymphoma
connects-toHepatic Lobule
connects-toMyelofibrosis
connects-toDengue Fever
connects-toWaldenstrom Macroglobulinemia
connects-toHiv 1
connects-toIfn Gamma
connects-toBaff
connects-toPerforin
connects-toIl 6
connects-toTnf Alpha
connects-toPf4
connects-toIl 2
connects-toMhc Class Ii
connects-toMpl
connects-toCaspase 3
connects-toCcl2
connects-toGlucocorticoid Receptor
connects-toBcl 2
connects-toSrc Kinase
connects-toIl 10
connects-toCtla 4
connects-toIl 17A
connects-toJak1 2
connects-toIl 12
connects-toPd 1
connects-toAkt
connects-toMtor
connects-toGalectin 3
connects-toStat1
connects-toCgas Sting
connects-toPik3Ca
connects-toFoxo
connects-toSmad4
connects-toS100A8 A9
connects-toGsk 3B
connects-toErk1 2
connects-toAutophagy
connects-toAmpk
connects-toCcr5
connects-toDnmt3A
connects-toCxcl12
connects-toIl 33
connects-toIl 1B
connects-toArid1A
connects-toCalcineurin
connects-toAdenosine
connects-toHemoglobin
connects-toIl 4
connects-toEstrogen
connects-toAdamts13
connects-toSerotonin
connects-toIl 13
connects-toFibrinogen
connects-toProstaglandins
connects-toNitric Oxide
connects-toTgf Beta
connects-toVegf
connects-toType I Interferon
connects-toLeptin
connects-toAdiponectin
connects-toResistin
connects-toIl 23
connects-toIl 5
connects-toHepcidin
connects-toHepatocyte
connects-toIge
connects-toHistamine
connects-toNeutrophil
connects-toC5Ar1
connects-toSelenium
connects-toFactor H
connects-toC1 Esterase Inhibitor
connects-toTransferrin
connects-toTslp
connects-toBradykinin
connects-toErythropoietin
connects-toPeriostin
connects-toMelatonin
connects-toProlactin
connects-toTestosterone
connects-toOxytocin
connects-toVasopressin
connects-toIodine
connects-toSodium
connects-toMagnesium
connects-toCopper
connects-toZinc
connects-toPotassium
connects-toCalcium
connects-toPhosphorus
connects-toChloride
connects-toCarbon
connects-toNitrogen
connects-toOxygen
connects-toHydrogen
connects-toSulfur
connects-toGlp 1
connects-toAngiotensin Ii
connects-toWnt Beta Catenin
connects-toRankl
connects-toFibronectin
connects-toNotch
connects-toIgf 1
connects-toActivin A
connects-toCgrp
connects-toCalcitonin
connects-toSubstance P
connects-toInsulin Receptor
connects-toAldosterone
connects-toAndrogen Receptor
connects-toNorepinephrine
connects-toAdrenomedullin
connects-toBdnf
connects-toOsteopontin
connects-toFgfr
Sources
- Cines DB, Blanchette VS. Immune thrombocytopenic purpura. N Engl J Med. 2002;346(13):995-1008. · PubMed 11919310
- Neunert C, Terrell DR, Arnold DM, et al. American Society of Hematology 2019 guidelines for immune thrombocytopenia. Blood Adv. 2019;3(23):3829-3866. · PubMed 31794604
- Bussel JB, Kuter DJ, George JN, et al. AMG 531, a thrombopoiesis-stimulating protein, for chronic ITP. N Engl J Med. 2006;355(16):1672-1681. · PubMed 17050891
- Cheng G, Saleh MN, Marcher C, et al. Eltrombopag for management of chronic immune thrombocytopenia (RAISE). Lancet. 2011;377(9763):393-402. · PubMed 21237459