Atlas One · Host Biology · Scale 07 — System

Myelofibrosis

Myelofibrosis is a MPN with BM fibrosis, megakaryocyte dysplasia, and splenomegaly; drivers JAK2 V617F ~60%, CALR exon 9 ~20-25%, MPL ~8%; ruxolitinib (COMFORT-I/II), fedratinib, pacritinib, momelotinib (MOMENTUM) approved; allo-SCT is the only curative option.

Also known as: myelofibrosis, MF, PMF, primary myelofibrosis, post-ET MF, post-PV MF, myeloproliferative neoplasm fibrosis, JAK inhibitor myelofibrosis

Scale 07 — SystemScale
draftStatus
2026-06-06Last Reviewed
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myelofibrosis

Myelofibrosis

Myelofibrosis is a MPN with BM fibrosis, megakaryocyte dysplasia, and splenomegaly; drivers JAK2 V617F ~60%, CALR exon 9 ~20-25%, MPL ~8%; ruxolitinib (COMFORT-I/II), fedratinib, pacritinib, momelotinib (MOMENTUM) approved; allo-SCT is the only curative option.