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polycythemia-vera
Polycythemia Vera
Polycythemia vera is a JAK2-driven MPN with erythrocytosis, thrombocytosis, and leukocytosis; JAK2 V617F ~99%; phlebotomy + low-dose aspirin for all; hydroxyurea or ropeginterferon alfa-2b for high-risk; ruxolitinib for HU-resistant; MF/AML transformation risk.
Entry Metadata
| Field | Value |
|---|---|
| ID | polycythemia-vera |
| Name | Polycythemia Vera |
| Status | draft |
| Last reviewed | 2026-06-06 |
| Atlas | 01-human |
| Scale | 07-system |
Cross-Atlas Connections
connects-toEpas1
connects-toJak2
connects-toErythropoietin
connects-toTgf Beta
connects-toMyeloproliferative Neoplasms
connects-toErythrocyte
connects-toSpleen
connects-toStroke
connects-toEssential Thrombocythemia
connects-toBone Marrow
connects-toMyelofibrosis
connects-toVenous Thromboembolism
connects-toAml
connects-toGout
connects-toCkd
connects-toRenal Cell Carcinoma
connects-toOxygen
connects-toIron Deficiency Anemia
connects-toCml
connects-toIron
connects-toPlatelet
connects-toCardiovascular System
connects-toLiver
connects-toMast Cell
connects-toStat3
connects-toHemoglobin
connects-toHistamine
connects-toNeutrophil
connects-toBrain
connects-toSkin
connects-toPotassium
connects-toHeart
connects-toEye
connects-toEndothelial Cell
connects-toElectron
connects-toKidney
connects-toLung
connects-toNeuron
connects-toJak1 2
connects-toVhl Disease
connects-toPhosphorus
connects-toHepatocyte
connects-toReproductive System
connects-toAtherosclerosis
connects-toOsteoblast
connects-toAkt
connects-toHepcidin
connects-toTet2
connects-toPulmonary Arterial Hypertension
connects-toNlrp3 Inflammasome
connects-toMds
connects-toHypertension
connects-toTnf Alpha
connects-toNf Kb
connects-toAnemia Of Chronic Disease
connects-toHeart Failure
connects-toMajor Depressive Disorder
connects-toSepsis
connects-toVaricella Zoster Virus
connects-toAspergillus Fumigatus
connects-toGeneralized Anxiety Disorder
connects-toIntegumentary System
connects-toDigestive System
connects-toNervous System
connects-toLymphatic System
connects-toRespiratory System
connects-toEndocrine System
connects-toAspirin
connects-toMusculoskeletal System
connects-toRenal System
connects-toTargeted Therapy
connects-toCancer Chemotherapy
connects-toMycobacterium Tuberculosis
connects-toArterial Wall
connects-toHepatic Lobule
connects-toCopd
connects-toMyocardium
connects-toAntiphospholipid Syndrome
connects-toPeripheral Nerve
connects-toVon Willebrand Factor
connects-toHcc
connects-toPheochromocytoma Paraganglioma
connects-toType I Interferon
connects-toHif 1Alpha
connects-toEzh2
connects-toIl 6
connects-toIl 1B
connects-toVegf
connects-toPf4
connects-toXanthine Oxidase
connects-toPdgf
connects-toCalr
connects-toThrombin
connects-toSf3B1
connects-toErk1 2
connects-toDnmt3A
connects-toFerroportin
connects-toPik3Ca
connects-toMtor
connects-toP53
connects-toMyd88
connects-toCdkn2A
connects-toRunx1
connects-toStat1
connects-toGalectin 3
connects-toPten
connects-toCgas Sting
connects-toSmad4
connects-toCdk4 6
connects-toFoxo
connects-toGsk 3B
connects-toS100A8 A9
connects-toSrc Kinase
connects-toMdm2
connects-toPerforin
connects-toAmpk
connects-toAutophagy
connects-toCcr5
connects-toCxcl12
connects-toArid1A
connects-toIl 33
connects-toEgln1
connects-toTransferrin
connects-toNitric Oxide
connects-toTroponin Complex
connects-toSerotonin
connects-toEndothelin 1
connects-toAdamts13
connects-toProtein C
connects-toIl 10
connects-toProstaglandins
connects-toAngiopoietin
connects-toFibrinogen
connects-toIl 4
connects-toLeptin
connects-toAdiponectin
connects-toIl 13
connects-toResistin
connects-toMacrophage
connects-toT Cytotoxic Cell
connects-toIfn Gamma
connects-toIl 12
connects-toIl 5
connects-toIl 23
connects-toIge
connects-toDendritic Cell
connects-toComplement C5
connects-toC5Ar1
connects-toComplement C3
connects-toFactor H
connects-toNatural Killer Cell
connects-toTslp
connects-toBradykinin
connects-toC1 Esterase Inhibitor
connects-toPeriostin
connects-toMelatonin
connects-toProlactin
connects-toTestosterone
connects-toOxytocin
connects-toVasopressin
connects-toSelenium
connects-toIodine
connects-toSodium
connects-toMagnesium
connects-toCopper
connects-toCalcium
connects-toZinc
connects-toChloride
connects-toSulfur
connects-toCarbon
connects-toHydrogen
connects-toNitrogen
connects-toPd 1
connects-toGlp 1
connects-toAngiotensin Ii
connects-toWnt Beta Catenin
connects-toRankl
connects-toIl 2
connects-toFibronectin
connects-toNotch
connects-toIgf 1
connects-toActivin A
connects-toCgrp
connects-toCalcitonin
connects-toSubstance P
connects-toInsulin Receptor
connects-toAldosterone
connects-toAndrogen Receptor
connects-toNorepinephrine
connects-toAdrenomedullin
connects-toBdnf
connects-toOsteopontin
connects-toFgfr
Sources
- Vannucchi AM, Kiladjian JJ, Griesshammer M, et al. Ruxolitinib versus standard therapy for the treatment of polycythemia vera. N Engl J Med. 2015;372(5):426-435. · PubMed 25577388
- Gisslinger H, Gotic M, Holowiecki J, et al. Ropeginterferon alfa-2b versus standard therapy for polycythaemia vera (PROUD-PV and CONTINUATION-PV): a randomised, non-inferiority, phase 3 trial and its extension study. Lancet Haematol. 2020;7(3):e196-e208. · PubMed 32046833