Atlas One · Host Biology · Scale 07 — System

Pheochromocytoma/Paraganglioma

Pheochromocytoma/paraganglioma are chromaffin cell tumors; ~40% hereditary (SDHx, VHL, RET, NF1); biochemical diagnosis: plasma/urine metanephrines; sunitinib (FIRSTMAPPP) and 177Lu-DOTATATE for metastatic disease; alpha-adrenergic blockade mandatory preoperatively.

Also known as: pheochromocytoma, paraganglioma, PHEO, PGL, PHEO/PGL, chromaffin tumor, hereditary paraganglioma, catecholamine-secreting tumor, adrenal pheochromocytoma, head-neck paraganglioma, SDHx tumor, MEN2 pheochromocytoma

Scale 07 — SystemScale
draftStatus
2026-06-06Last Reviewed
This is an auto-generated stub page built from atlas entry frontmatter. A richer hand-crafted page is planned. See the atlas source for the full entry including detailed body sections.
pheochromocytoma-paraganglioma

Pheochromocytoma/Paraganglioma

Pheochromocytoma/paraganglioma are chromaffin cell tumors; ~40% hereditary (SDHx, VHL, RET, NF1); biochemical diagnosis: plasma/urine metanephrines; sunitinib (FIRSTMAPPP) and 177Lu-DOTATATE for metastatic disease; alpha-adrenergic blockade mandatory preoperatively.

Entry Metadata

FieldValue
IDpheochromocytoma-paraganglioma
NamePheochromocytoma/Paraganglioma
Statusdraft
Last reviewed2026-06-06
Atlas01-human
Scale07-system

Cross-Atlas Connections

connects-toSdhb connects-toVhl connects-toRet connects-toHif 1Alpha connects-toAdrenal Gland connects-toNeurofibromatosis Type 1 connects-toEpinephrine connects-toRenal Cell Carcinoma connects-toVhl Disease connects-toNeuroblastoma connects-toHypertension connects-toCarney Complex connects-toHlrcc connects-toNorepinephrine connects-toPanic Disorder connects-toGist connects-toNf1 connects-toHeart connects-toMen1 Syndrome connects-toCardiovascular System connects-toNervous System connects-toEndocrine System connects-toIodine connects-toSstr2 connects-toNeuron connects-toDopamine connects-toOxygen connects-toVegf connects-toCalcium connects-toMacrophage connects-toKidney connects-toBrain connects-toCardiomyocyte connects-toPotassium connects-toPhoton connects-toElectron connects-toBone Marrow connects-toErythrocyte connects-toLiver connects-toSkin connects-toAntibody connects-toStroke connects-toMagnesium connects-toReproductive System connects-toThyroid Cancer connects-toAkt connects-toType 2 Diabetes connects-toTert connects-toEndothelial Cell connects-toEpas1 connects-toFh connects-toHeart Failure connects-toStat3 connects-toSepsis connects-toCkd connects-toVenous Thromboembolism connects-toMajor Depressive Disorder connects-toPulmonary Arterial Hypertension connects-toWound Healing connects-toAtherosclerosis connects-toDigestive System connects-toIntegumentary System connects-toRespiratory System connects-toMusculoskeletal System connects-toRenal System connects-toLymphatic System connects-toBeta Blockers connects-toCalcium Channel Blockers connects-toTargeted Therapy connects-toNeuroendocrine Tumors connects-toCancer Chemotherapy connects-toPolycythemia Vera connects-toCheckpoint Inhibitors connects-toMyocardium connects-toCardiac Conduction System connects-toIdh Mutant Glioma connects-toArterial Wall connects-toGlomerulus connects-toMen4 Syndrome connects-toCortical Bone connects-toHepatic Lobule connects-toCovid 19 Disease connects-toEzh2 connects-toKras connects-toPdgf connects-toErk1 2 connects-toMyc connects-toCyclin D1 connects-toEgln1 connects-toWnt Beta Catenin connects-toAtrx connects-toMtor connects-toBeta1 Adrenergic Receptor connects-toIdh1 connects-toPik3Ca connects-toTroponin Complex connects-toInsulin connects-toPten connects-toNfe2L2 connects-toE2F1 connects-toIdh2 connects-toRb1 connects-toJak1 2 connects-toGalectin 3 connects-toTgf Beta connects-toCgas Sting connects-toStat1 connects-toSmad4 connects-toFoxo connects-toGsk 3B connects-toMdm2 connects-toPerforin connects-toS100A8 A9 connects-toDnmt3A connects-toAutophagy connects-toAmpk connects-toCcr5 connects-toSrc Kinase connects-toArid1A connects-toCxcl12 connects-toIl 6 connects-toAcetylcholine connects-toNpy connects-toCalcium connects-toErythropoietin connects-toMhc Class Ii connects-toIl 2 connects-toPeripheral Nerve connects-toHemoglobin connects-toAldosterone connects-toAngiotensin Ii connects-toRenin connects-toIl 10 connects-toT Cytotoxic Cell connects-toIl 4 connects-toIl 13 connects-toCopper connects-toLeptin connects-toAdiponectin connects-toResistin connects-toIron connects-toType I Interferon connects-toIfn Gamma connects-toIl 12 connects-toIl 5 connects-toIl 17A connects-toIl 23 connects-toIge connects-toT Helper Cell connects-toMast Cell connects-toComplement C3 connects-toTslp connects-toHistamine connects-toBradykinin connects-toC1 Esterase Inhibitor connects-toPeriostin connects-toComplement C5 connects-toMelatonin connects-toTestosterone connects-toSerotonin connects-toOxytocin connects-toVasopressin connects-toProlactin connects-toSelenium connects-toSodium connects-toZinc connects-toChloride connects-toSulfur connects-toNitrogen connects-toCarbon connects-toHydrogen connects-toPhosphorus connects-toPd 1 connects-toGlp 1 connects-toRankl connects-toFibronectin connects-toNotch connects-toIgf 1 connects-toActivin A connects-toCgrp connects-toCalcitonin connects-toSubstance P connects-toInsulin Receptor connects-toAndrogen Receptor connects-toAdrenomedullin connects-toBdnf connects-toOsteopontin connects-toFgfr connects-toMyostatin connects-toAngiopoietin connects-toCortisol connects-toGhrelin connects-toGlucagon