Atlas One · Host Biology · Scale 07 — System

Pheochromocytoma/Paraganglioma

Pheochromocytoma/paraganglioma are chromaffin cell tumors; ~40% hereditary (SDHx, VHL, RET, NF1); biochemical diagnosis: plasma/urine metanephrines; sunitinib (FIRSTMAPPP) and 177Lu-DOTATATE for metastatic disease; alpha-adrenergic blockade mandatory preoperatively.

Also known as: pheochromocytoma, paraganglioma, PHEO, PGL, PHEO/PGL, chromaffin tumor, hereditary paraganglioma, catecholamine-secreting tumor, adrenal pheochromocytoma, head-neck paraganglioma, SDHx tumor, MEN2 pheochromocytoma

Scale 07 — SystemScale
draftStatus
2026-06-06Last Reviewed
This is an auto-generated stub page built from atlas entry frontmatter. A richer hand-crafted page is planned. See the atlas source for the full entry including detailed body sections.
pheochromocytoma-paraganglioma

Pheochromocytoma/Paraganglioma

Pheochromocytoma/paraganglioma are chromaffin cell tumors; ~40% hereditary (SDHx, VHL, RET, NF1); biochemical diagnosis: plasma/urine metanephrines; sunitinib (FIRSTMAPPP) and 177Lu-DOTATATE for metastatic disease; alpha-adrenergic blockade mandatory preoperatively.

Entry Metadata

FieldValue
IDpheochromocytoma-paraganglioma
NamePheochromocytoma/Paraganglioma
Statusdraft
Last reviewed2026-06-06
Atlas01-human
Scale07-system

Cross-Atlas Connections

connects-toSdhb connects-toVhl connects-toRet connects-toHif 1Alpha connects-toAdrenal Gland connects-toNeurofibromatosis Type 1 connects-toEpinephrine connects-toRenal Cell Carcinoma connects-toVhl Disease connects-toNeuroblastoma

Sources