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neuroblastoma
Neuroblastoma
Neuroblastoma is the most common extracranial pediatric solid tumor; neural crest-derived; MYCN amplification in ~40% high-risk; tandem auto-SCT + dinutuximab (anti-GD2) + 13-cis-retinoic acid maintenance for high-risk; ALK inhibitors in Phase 3 trials.
Entry Metadata
| Field | Value |
|---|---|
| ID | neuroblastoma |
| Name | Neuroblastoma |
| Status | draft |
| Last reviewed | 2026-06-06 |
| Atlas | 01-human |
| Scale | 07-system |
Cross-Atlas Connections
connects-toMycn
connects-toAlk
connects-toRet
connects-toP53
connects-toNtrk
connects-toAdrenal Gland
connects-toNatural Killer Cell
connects-toNeuroendocrine Tumors
connects-toBone Marrow
connects-toNeuron
connects-toPheochromocytoma Paraganglioma
connects-toWilms Tumor
connects-toPhoton
connects-toEwing Sarcoma
connects-toMedulloblastoma
connects-toLi Fraumeni Syndrome
connects-toNorepinephrine
connects-toNervous System
connects-toLiver
connects-toImmune System
connects-toProton
connects-toT Cytotoxic Cell
connects-toIodine
connects-toTert
connects-toMacrophage
connects-toDopamine
connects-toRegulatory T Cell
connects-toVegf
connects-toSkin
connects-toDendritic Cell
connects-toAkt
connects-toEye
connects-toCalcium
connects-toEndothelial Cell
connects-toElectron
connects-toKidney
connects-toLung
connects-toBrain
connects-toLarge Intestine
connects-toPotassium
connects-toAntibody
connects-toNeutrophil
connects-toErythrocyte
connects-toPlatelet
connects-toMagnesium
connects-toReproductive System
connects-toAtrx
connects-toPeripheral Nerve
connects-toHypertension
connects-toCdkn2A
connects-toNeuropathic Pain
connects-toSepsis
connects-toStat3
connects-toVenous Thromboembolism
connects-toAnemia Of Chronic Disease
connects-toHeart Failure
connects-toAspergillus Fumigatus
connects-toCkd
connects-toVaricella Zoster Virus
connects-toWound Healing
connects-toGeneralized Anxiety Disorder
connects-toMusculoskeletal System
connects-toDigestive System
connects-toEndocrine System
connects-toIntegumentary System
connects-toRespiratory System
connects-toLymphatic System
connects-toCardiovascular System
connects-toRenal System
connects-toTargeted Therapy
connects-toCancer Chemotherapy
connects-toCar T
connects-toMpnst
connects-toCortical Bone
connects-toDiffuse Midline Glioma
connects-toCheckpoint Inhibitors
connects-toHepatic Lobule
connects-toRetinoblastoma
connects-toRhabdomyosarcoma
connects-toNsclc
connects-toAml
connects-toMyocardium
connects-toBcl 2
connects-toCdk4 6
connects-toEzh2
connects-toMyc
connects-toMtor
connects-toHif 1Alpha
connects-toErk1 2
connects-toCaspase 3
connects-toCcl2
connects-toCxcl12
connects-toPerforin
connects-toCgas Sting
connects-toBdnf
connects-toWnt Beta Catenin
connects-toDnmt3A
connects-toPik3Ca
connects-toE2F1
connects-toKras
connects-toRb1
connects-toMdm2
connects-toJak1 2
connects-toGalectin 3
connects-toTgf Beta
connects-toPten
connects-toStat1
connects-toSmad4
connects-toFoxo
connects-toGsk 3B
connects-toS100A8 A9
connects-toSrc Kinase
connects-toAutophagy
connects-toArid1A
connects-toAmpk
connects-toCcr5
connects-toIl 6
connects-toNotch
connects-toIl 1B
connects-toIl 33
connects-toIl 17A
connects-toComplement C3
connects-toCalcineurin
connects-toOsteopontin
connects-toIl 2
connects-toMhc Class Ii
connects-toPd 1
connects-toHemoglobin
connects-toTroponin Complex
connects-toIl 10
connects-toIl 4
connects-toXanthine Oxidase
connects-toIron
connects-toIl 13
connects-toCopper
connects-toNitric Oxide
connects-toLeptin
connects-toAdiponectin
connects-toResistin
connects-toType I Interferon
connects-toIfn Gamma
connects-toIl 12
connects-toIl 5
connects-toIl 23
connects-toIge
connects-toB Cell
connects-toMast Cell
connects-toT Helper Cell
connects-toComplement C5
connects-toC5Ar1
connects-toFactor H
connects-toErythropoietin
connects-toHistamine
connects-toBradykinin
connects-toTslp
connects-toC1 Esterase Inhibitor
connects-toPeriostin
connects-toMelatonin
connects-toTestosterone
connects-toSerotonin
connects-toProlactin
connects-toOxytocin
connects-toVasopressin
connects-toSelenium
connects-toSodium
connects-toZinc
connects-toPhosphorus
connects-toOxygen
connects-toChloride
connects-toCarbon
connects-toHydrogen
connects-toNitrogen
connects-toSulfur
connects-toGlp 1
connects-toAngiotensin Ii
connects-toRankl
connects-toFibronectin
connects-toIgf 1
connects-toActivin A
connects-toCgrp
connects-toCalcitonin
connects-toSubstance P
connects-toInsulin Receptor
connects-toAldosterone
connects-toAndrogen Receptor
connects-toAdrenomedullin
connects-toFgfr
connects-toEpinephrine
connects-toRenin
connects-toMyostatin
connects-toAngiopoietin
connects-toCortisol
connects-toGhrelin
Sources
- Yu AL, Gilman AL, Ozkaynak MF, et al. Anti-GD2 antibody with GM-CSF, interleukin-2, and isotretinoin for neuroblastoma. N Engl J Med. 2010;363(14):1324-1334. · PubMed 20879881
- Park JR, Kreissman SG, London WB, et al. Effect of tandem autologous stem cell transplant vs single transplant on event-free survival in patients with high-risk neuroblastoma: a randomized clinical trial. JAMA. 2019;322(8):746-755. · PubMed 31454023