Atlas One · Host Biology · Scale 07 — System

Rhabdomyosarcoma

Rhabdomyosarcoma is the most common pediatric soft tissue sarcoma; embryonal (~60%, VAC backbone, 5-year FFS ~90% low-risk) and alveolar (~25%, PAX3/PAX7-FOXO1 fusions, high-risk) subtypes; VAC±irinotecan; RT; metastatic disease 5-year OS ~20-30%.

Also known as: rhabdomyosarcoma, RMS, embryonal RMS, alveolar RMS, ERMS, ARMS, pediatric soft tissue sarcoma, botryoid RMS

Scale 07 — SystemScale
draftStatus
2026-06-06Last Reviewed
This is an auto-generated stub page built from atlas entry frontmatter. A richer hand-crafted page is planned. See the atlas source for the full entry including detailed body sections.
rhabdomyosarcoma

Rhabdomyosarcoma

Rhabdomyosarcoma is the most common pediatric soft tissue sarcoma; embryonal (~60%, VAC backbone, 5-year FFS ~90% low-risk) and alveolar (~25%, PAX3/PAX7-FOXO1 fusions, high-risk) subtypes; VAC±irinotecan; RT; metastatic disease 5-year OS ~20-30%.

Entry Metadata

FieldValue
IDrhabdomyosarcoma
NameRhabdomyosarcoma
Statusdraft
Last reviewed2026-06-06
Atlas01-human
Scale07-system

Cross-Atlas Connections

connects-toFoxo1 connects-toMyc connects-toAkt connects-toMet connects-toLi Fraumeni Syndrome connects-toIgf 1 connects-toDicer1 connects-toWilms Tumor connects-toMusculoskeletal System connects-toNeuroblastoma connects-toEwing Sarcoma connects-toDicer1 Syndrome connects-toNoonan Syndrome connects-toOsteosarcoma connects-toSynovial Sarcoma connects-toPhoton connects-toNeurofibromatosis Type 1 connects-toFibroblast connects-toP53 connects-toProton connects-toNervous System connects-toLung connects-toBone Marrow connects-toCardiomyocyte connects-toMtor connects-toKras connects-toSmo connects-toMacrophage connects-toOxygen connects-toBrain connects-toT Cytotoxic Cell connects-toEye connects-toCalcium connects-toEndothelial Cell connects-toElectron connects-toKidney connects-toLiver connects-toNeuron connects-toHeart connects-toBladder Cancer connects-toAntibody connects-toNeutrophil connects-toReproductive System connects-toMagnesium connects-toCdk4 6 connects-toPlatelet connects-toMycn connects-toNatural Killer Cell connects-toRegulatory T Cell connects-toCdkn2A connects-toNeuropathic Pain connects-toSepsis connects-toStat3 connects-toAml connects-toCkd connects-toHeart Failure connects-toAspergillus Fumigatus connects-toMajor Depressive Disorder connects-toWound Healing connects-toVaricella Zoster Virus connects-toGeneralized Anxiety Disorder connects-toRespiratory System connects-toEndocrine System connects-toDigestive System connects-toLymphatic System connects-toRenal System connects-toCardiovascular System connects-toImmune System connects-toIntegumentary System connects-toTargeted Therapy connects-toCancer Chemotherapy connects-toGist connects-toCheckpoint Inhibitors connects-toAlveolus connects-toGorlin Syndrome connects-toMedulloblastoma connects-toRetinoblastoma connects-toCortical Bone connects-toPeripheral Nerve connects-toCervical Cancer connects-toDesmoid Tumor connects-toMpnst connects-toFgfr connects-toYap1 connects-toNotch connects-toCyclin D1 connects-toPdgf connects-toHif 1Alpha connects-toEzh2 connects-toCxcl12 connects-toMyostatin connects-toNtrk connects-toWnt Beta Catenin connects-toCcl2 connects-toPik3Ca connects-toTgf Beta connects-toCaspase 3 connects-toErk1 2 connects-toE2F1 connects-toPten connects-toRb1 connects-toMdm2 connects-toJak1 2 connects-toGalectin 3 connects-toSmad4 connects-toCgas Sting connects-toStat1 connects-toPerforin connects-toSrc Kinase connects-toGsk 3B connects-toS100A8 A9 connects-toFoxo connects-toDnmt3A connects-toAutophagy connects-toArid1A connects-toAmpk connects-toCcr5 connects-toIl 6 connects-toIl 1B connects-toIl 33 connects-toIl 17A connects-toTroponin Complex connects-toRankl connects-toMhc Class Ii connects-toIl 2 connects-toHemoglobin connects-toPd 1 connects-toXanthine Oxidase connects-toIl 10 connects-toNitric Oxide connects-toIl 4 connects-toIron connects-toProstaglandins connects-toIl 13 connects-toMacrophage connects-toCortical Bone connects-toLeptin connects-toAdiponectin connects-toResistin connects-toType I Interferon connects-toIfn Gamma connects-toIl 12 connects-toIl 5 connects-toIl 23 connects-toIge connects-toMast Cell connects-toDendritic Cell connects-toT Helper Cell connects-toB Cell connects-toComplement C3 connects-toC5Ar1 connects-toTslp connects-toPeriostin connects-toErythropoietin connects-toBradykinin connects-toC1 Esterase Inhibitor connects-toHistamine connects-toMelatonin connects-toTestosterone connects-toSerotonin connects-toOxytocin connects-toVasopressin connects-toProlactin connects-toSelenium connects-toIodine connects-toSodium connects-toCopper connects-toZinc connects-toPotassium connects-toCarbon connects-toChloride connects-toHydrogen connects-toNitrogen connects-toPhosphorus connects-toSulfur connects-toGlp 1 connects-toAngiotensin Ii connects-toVegf connects-toFibronectin connects-toActivin A connects-toCgrp connects-toCalcitonin connects-toSubstance P connects-toInsulin Receptor connects-toAldosterone connects-toAndrogen Receptor connects-toNorepinephrine connects-toAdrenomedullin connects-toBdnf connects-toOsteopontin connects-toEpinephrine connects-toRenin connects-toAngiopoietin