Atlas One · Host Biology · Scale 07 — System

Retinoblastoma

Retinoblastoma is the most common intraocular childhood tumor (1/15,000); bilateral = germline RB1; unilateral = usually somatic; leukocoria is the classic presentation; intra-arterial/intravitreal chemotherapy preserves vision; hereditary RB1 confers osteosarcoma risk.

Also known as: retinoblastoma, RB1 tumor, bilateral retinoblastoma, hereditary retinoblastoma, RBL, retinoblastoma leukocoria, intraocular tumor child, retinoblastoma treatment, retinoblastoma genetics

Scale 07 — SystemScale
draftStatus
2026-06-07Last Reviewed
This is an auto-generated stub page built from atlas entry frontmatter. A richer hand-crafted page is planned. See the atlas source for the full entry including detailed body sections.
retinoblastoma

Retinoblastoma

Retinoblastoma is the most common intraocular childhood tumor (1/15,000); bilateral = germline RB1; unilateral = usually somatic; leukocoria is the classic presentation; intra-arterial/intravitreal chemotherapy preserves vision; hereditary RB1 confers osteosarcoma risk.

Entry Metadata

FieldValue
IDretinoblastoma
NameRetinoblastoma
Statusdraft
Last reviewed2026-06-07
Atlas01-human
Scale07-system

Cross-Atlas Connections

connects-toE2F1 connects-toRb1 connects-toP53 connects-toOsteosarcoma connects-toEye connects-toMycn connects-toMdm2 connects-toNeuron connects-toBrain connects-toLi Fraumeni Syndrome connects-toPhoton connects-toSclc connects-toMelanoma connects-toUveal Melanoma connects-toNeuroblastoma connects-toMedulloblastoma connects-toCdk4 6 connects-toBone Marrow connects-toBreast Cancer connects-toProton connects-toNervous System connects-toCdkn2A connects-toCyclin D1 connects-toIodine connects-toAstrocyte connects-toMelatonin connects-toVegf connects-toMacrophage connects-toCalcium connects-toT Cytotoxic Cell connects-toLiver connects-toPhosphorus connects-toEndothelial Cell connects-toSkin connects-toElectron connects-toMicroglia connects-toLung connects-toCollagen connects-toErythrocyte connects-toMagnesium connects-toAntibody connects-toNeutrophil connects-toReproductive System connects-toThyroid Cancer connects-toPlatelet connects-toKidney connects-toTert connects-toBladder Cancer connects-toNatural Killer Cell connects-toSepsis connects-toStroke connects-toVenous Thromboembolism connects-toAml connects-toCkd connects-toAnemia Of Chronic Disease connects-toRhabdomyosarcoma connects-toAspergillus Fumigatus connects-toMajor Depressive Disorder connects-toWound Healing connects-toVaricella Zoster Virus connects-toGeneralized Anxiety Disorder connects-toMusculoskeletal System connects-toDigestive System connects-toIntegumentary System connects-toRenal System connects-toEndocrine System connects-toRespiratory System connects-toCardiovascular System connects-toImmune System connects-toLymphatic System connects-toCancer Chemotherapy connects-toTargeted Therapy connects-toCortical Bone connects-toGlioblastoma connects-toSynapse connects-toCar T connects-toAxonal Transport connects-toWilms Tumor connects-toHepatic Lobule connects-toMeningioma connects-toProstate Cancer connects-toSynovial Sarcoma connects-toMyc connects-toBcl 2 connects-toEzh2 connects-toAkt connects-toMtor connects-toHif 1Alpha connects-toCaspase 3 connects-toCxcl12 connects-toOsteopontin connects-toNotch connects-toCcl2 connects-toBdnf connects-toPik3Ca connects-toIgf 1 connects-toDnmt3A connects-toPten connects-toErk1 2 connects-toStat3 connects-toKras connects-toJak1 2 connects-toNf Kb connects-toGalectin 3 connects-toTgf Beta connects-toCgas Sting connects-toStat1 connects-toSmad4 connects-toFoxo connects-toGsk 3B connects-toPerforin connects-toS100A8 A9 connects-toSrc Kinase connects-toAutophagy connects-toArid1A connects-toAmpk connects-toCcr5 connects-toIl 6 connects-toIl 1B connects-toIl 33 connects-toIl 17A connects-toNtrk connects-toThyroid Hormones connects-toMhc Class Ii connects-toIl 2 connects-toPd 1 connects-toHemoglobin connects-toTroponin Complex connects-toIl 10 connects-toXanthine Oxidase connects-toIl 4 connects-toIron connects-toNitric Oxide connects-toIl 13 connects-toProstaglandins connects-toHepcidin connects-toLeptin connects-toAdiponectin connects-toResistin connects-toType I Interferon connects-toIfn Gamma connects-toIl 12 connects-toIl 5 connects-toIl 23 connects-toIge connects-toMast Cell connects-toDendritic Cell connects-toT Helper Cell connects-toB Cell connects-toComplement C3 connects-toC5Ar1 connects-toErythropoietin connects-toHistamine connects-toBradykinin connects-toTslp connects-toC1 Esterase Inhibitor connects-toPeriostin connects-toTestosterone connects-toSerotonin connects-toProlactin connects-toOxytocin connects-toVasopressin connects-toSelenium connects-toSodium connects-toCopper connects-toZinc connects-toPotassium connects-toChloride connects-toSulfur connects-toCarbon connects-toHydrogen connects-toNitrogen connects-toOxygen connects-toGlp 1 connects-toAngiotensin Ii connects-toWnt Beta Catenin connects-toRankl connects-toFibronectin connects-toActivin A connects-toCgrp connects-toCalcitonin connects-toSubstance P connects-toInsulin Receptor connects-toAldosterone connects-toAndrogen Receptor connects-toNorepinephrine connects-toAdrenomedullin connects-toFgfr connects-toEpinephrine connects-toRenin connects-toMyostatin connects-toAngiopoietin connects-toCortisol