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medulloblastoma
Medulloblastoma
Medulloblastoma is the most common pediatric brain tumor; 4 molecular subgroups: WNT (~10%, OS ~95%), SHH (~38%), Group 3 (~25%, MYC-amplified, worst prognosis), Group 4 (~35%); surgery + CSI + chemotherapy; SHH MB responsive to SMO inhibitors; infant MB: chemo without radiation.
Entry Metadata
| Field | Value |
|---|---|
| ID | medulloblastoma |
| Name | Medulloblastoma |
| Status | draft |
| Last reviewed | 2026-06-06 |
| Atlas | 01-human |
| Scale | 07-system |
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Sources
- Packer RJ, Gajjar A, Vezina G, et al. Phase III study of craniospinal radiation therapy followed by adjuvant chemotherapy for newly diagnosed average-risk medulloblastoma. J Clin Oncol. 2006;24(25):4202-4208. · PubMed 16943538
- Taylor MD, Northcott PA, Korshunov A, et al. Molecular subgroups of medulloblastoma: the current consensus. Acta Neuropathol. 2012;123(4):465-472. · PubMed 22134537