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cidp
CIDP
CIDP (chronic inflammatory demyelinating polyneuropathy) is immune-mediated PNS demyelination lasting >8 weeks; anti-NF155/CNTN1 IgG4 define subtypes; IVIG and corticosteroids first-line; efgartigimod (FcRn inhibitor; FDA Jun 2024) and inebilizumab (anti-CD19) are new options.
Entry Metadata
| Field | Value |
|---|---|
| ID | cidp |
| Name | CIDP |
| Status | draft |
| Last reviewed | 2026-06-07 |
| Atlas | 01-human |
| Scale | 07-system |
Cross-Atlas Connections
connects-toFcrn
modulated-byImmunoglobulin G
connects-toPeripheral Nerve
connects-toIl 2
connects-toGuillain Barre
connects-toMacrophage
connects-toTnf Alpha
connects-toAls
connects-toB Cell
connects-toMultiple Sclerosis
connects-toMyasthenia Gravis
connects-toType 2 Diabetes
connects-toNeuropathic Pain
connects-toPlasma Cell
connects-toRegulatory T Cell
connects-toNmo
connects-toT Helper Cell
connects-toComplement C5
connects-toType 1 Diabetes
connects-toNeuron
connects-toImmune System
connects-toNervous System
connects-toComplement C3
connects-toWaldenstrom Macroglobulinemia
connects-toT Cytotoxic Cell
connects-toCortisol
connects-toDendritic Cell
connects-toCd20
connects-toSodium
connects-toPotassium
connects-toNf Kb
connects-toKidney
connects-toVegf
connects-toCalcium
connects-toPhoton
connects-toBone Marrow
connects-toIl 6
connects-toElectron
connects-toLung
connects-toEye
connects-toAntibody
connects-toOligodendrocyte
connects-toMusculoskeletal System
connects-toHiv
connects-toEndothelial Cell
connects-toThymus
connects-toBaff
connects-toMultiple Myeloma
connects-toSjogrens Syndrome
connects-toIl 17A
connects-toNatural Killer Cell
connects-toHepatitis C
connects-toStat3
connects-toVenous Thromboembolism
connects-toSepsis
connects-toOsteoporosis
connects-toCkd
connects-toMajor Depressive Disorder
connects-toWound Healing
connects-toAspergillus Fumigatus
connects-toStroke
connects-toVaricella Zoster Virus
connects-toEndocrine System
connects-toGeneralized Anxiety Disorder
connects-toRespiratory System
connects-toRenal System
connects-toCardiovascular System
connects-toCorticosteroids
connects-toLymphatic System
connects-toReproductive System
connects-toCancer Chemotherapy
connects-toHiv 1
connects-toAnca Vasculitis
connects-toTargeted Therapy
connects-toAxonal Transport
connects-toSystemic Lupus Erythematosus
connects-toGerminal Center
connects-toRheumatoid Arthritis
connects-toInflammatory Bowel Disease
connects-toCheckpoint Inhibitors
connects-toMelanoma
connects-toCovid 19 Disease
connects-toCtla 4
connects-toBtk
connects-toJak1 2
connects-toIfn Gamma
connects-toIl 1B
connects-toNlrp3 Inflammasome
connects-toCcl2
connects-toMhc Class Ii
connects-toTgf Beta
connects-toTlr4
connects-toCxcl12
connects-toNtrk
connects-toGlucocorticoid Receptor
connects-toBcl 2
connects-toPerforin
connects-toIl 12
connects-toIl 23
connects-toIl 10
connects-toMyd88
connects-toC5Ar1
connects-toNfe2L2
connects-toAkt
connects-toMtor
connects-toGalectin 3
connects-toStat1
connects-toCgas Sting
connects-toSmad4
connects-toFoxo
connects-toErk1 2
connects-toS100A8 A9
connects-toGsk 3B
connects-toPik3Ca
connects-toHif 1Alpha
connects-toAmpk
connects-toAutophagy
connects-toCcr5
connects-toDnmt3A
connects-toSrc Kinase
connects-toIl 33
connects-toArid1A
connects-toCalcineurin
connects-toAdenosine
connects-toBdnf
connects-toIl 4
connects-toPd 1
connects-toIl 13
connects-toNitric Oxide
connects-toCollagen
connects-toProstaglandins
connects-toXanthine Oxidase
connects-toCholesterol
connects-toIgf 1
connects-toPdgf
connects-toCopper
connects-toType I Interferon
connects-toPlasma Cell
connects-toNmo
connects-toLeptin
connects-toAdiponectin
connects-toResistin
connects-toNeutrophil
connects-toIl 5
connects-toIge
connects-toMast Cell
connects-toVitamin D
connects-toSelenium
connects-toFactor H
connects-toC1 Esterase Inhibitor
connects-toTransferrin
connects-toOsteopontin
connects-toPeriostin
connects-toConnexin43
connects-toTslp
connects-toBradykinin
connects-toErythropoietin
connects-toHistamine
connects-toMelatonin
connects-toTestosterone
connects-toProlactin
connects-toOxytocin
connects-toVasopressin
connects-toSerotonin
connects-toIodine
connects-toMagnesium
connects-toSodium
connects-toZinc
connects-toPotassium
connects-toIron
connects-toPhosphorus
connects-toChloride
connects-toCarbon
connects-toHydrogen
connects-toNitrogen
connects-toGlp 1
connects-toAngiotensin Ii
connects-toWnt Beta Catenin
connects-toRankl
connects-toFibronectin
connects-toNotch
connects-toActivin A
connects-toCgrp
connects-toCalcitonin
connects-toSubstance P
connects-toInsulin Receptor
connects-toAldosterone
connects-toAndrogen Receptor
connects-toNorepinephrine
connects-toAdrenomedullin
connects-toFgfr
connects-toEpinephrine
connects-toRenin
Sources
- European Federation of Neurological Societies/Peripheral Nerve Society Guideline on management of chronic inflammatory demyelinating polyradiculoneuropathy. J Peripher Nerv Syst. 2010;15(1):1-9. · PubMed 20433600
- Hughes RA, Donofrio P, Bril V, et al. Intravenous immune globulin (10% caprylate-chromatography purified) for the treatment of chronic inflammatory demyelinating polyradiculoneuropathy (ICE study). Lancet Neurol. 2008;7(2):136-144. · PubMed 18178525
- van den Bergh PYK, van Doorn PA, Hadden RDM, et al. Efgartigimod alfa and hyaluronidase-qvfc in CIDP (ADHERE). N Engl J Med. 2023;390(3):219-232. · PubMed 38197812
- Van den Bergh PYK, van Doorn PA, Hadden RDM, et al. European Academy of Neurology/Peripheral Nerve Society guideline on diagnosis and treatment of chronic inflammatory demyelinating polyradiculoneuropathy: 2023 update. Eur J Neurol. 2023;30(10):2976-3020. · PubMed 37382198