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nmo
NMOSD
NMOSD: AQP4-IgG+ (85%) or MOG-IgG+ attacks on optic nerves, spinal cord, and brainstem (area postrema); relapsing; high morbidity. Eculizumab (PREVENT; FDA Jun 2019), inebilizumab (N-MOmentum; FDA Jun 2020), satralizumab (SAkuraStar; FDA Aug 2020) approved.
Entry Metadata
| Field | Value |
|---|---|
| ID | nmo |
| Name | NMOSD |
| Status | draft |
| Last reviewed | 2026-06-07 |
| Atlas | 01-human |
| Scale | 07-system |
Cross-Atlas Connections
connects-toAquaporin 4
connects-toComplement C5
connects-toIl 6
connects-toCd20
connects-toType I Interferon
connects-toAstrocyte
connects-toMultiple Sclerosis
connects-toEye
connects-toWest Nile Virus
connects-toB Cell
connects-toSjogrens Syndrome
connects-toSystemic Lupus Erythematosus
connects-toMyasthenia Gravis
connects-toPlasma Cell
connects-toGuillain Barre
connects-toComplement C3
connects-toOligodendrocyte
connects-toImmunoglobulin G
connects-toT Helper Cell
connects-toImmune System
connects-toBrain
connects-toRegulatory T Cell
connects-toNatural Killer Cell
connects-toNeutrophil
connects-toGlutamate
connects-toJak1 2
connects-toFcrn
connects-toIl 17A
connects-toMacrophage
connects-toCalcium
connects-toNeuron
connects-toSynapse
connects-toPhoton
connects-toSodium
connects-toEndothelial Cell
connects-toElectron
connects-toStomach
connects-toPotassium
connects-toAntibody
connects-toLung
connects-toKidney
connects-toLarge Intestine
connects-toReproductive System
connects-toHippocampus
connects-toMicroglia
connects-toBaff
connects-toRheumatoid Arthritis
connects-toNeuropathic Pain
connects-toEpilepsy
connects-toDendritic Cell
connects-toNf Kb
connects-toSepsis
connects-toVenous Thromboembolism
connects-toMajor Depressive Disorder
connects-toPneumocystis Jirovecii
connects-toOsteoporosis
connects-toWound Healing
connects-toCkd
connects-toAspergillus Fumigatus
connects-toNervous System
connects-toRespiratory System
connects-toNeisseria Meningitidis
connects-toDigestive System
connects-toEndocrine System
connects-toMusculoskeletal System
connects-toCardiovascular System
connects-toIntegumentary System
connects-toRenal System
connects-toTargeted Therapy
connects-toCorticosteroids
connects-toEpstein Barr Virus
connects-toCancer Chemotherapy
connects-toCheckpoint Inhibitors
connects-toAxonal Transport
connects-toPemphigus Vulgaris
connects-toBreast Cancer
connects-toImmune Thrombocytopenia
connects-toGerminal Center
connects-toAntiphospholipid Syndrome
connects-toSclc
connects-toCovid 19 Disease
connects-toType 1 Diabetes
connects-toNarcolepsy
connects-toIfn Gamma
connects-toPerforin
connects-toNlrp3 Inflammasome
connects-toIl 5
connects-toTgf Beta
connects-toMhc Class Ii
connects-toCcl2
connects-toIl 1B
connects-toTnf Alpha
connects-toC5Ar1
connects-toConnexin43
connects-toVegf
connects-toStat3
connects-toCaspase 3
connects-toBdnf
connects-toIl 23
connects-toIl 13
connects-toCtla 4
connects-toAkt
connects-toMtor
connects-toMyd88
connects-toGalectin 3
connects-toStat1
connects-toCgas Sting
connects-toFoxo
connects-toS100A8 A9
connects-toErk1 2
connects-toGsk 3B
connects-toHif 1Alpha
connects-toPik3Ca
connects-toSrc Kinase
connects-toAutophagy
connects-toAmpk
connects-toCcr5
connects-toDnmt3A
connects-toCxcl12
connects-toIl 33
connects-toArid1A
connects-toCalcineurin
connects-toPotassium
connects-toEstrogen
connects-toIl 2
connects-toIl 4
connects-toIl 10
connects-toProgesterone
connects-toNitric Oxide
connects-toXanthine Oxidase
connects-toProstaglandins
connects-toMagnesium
connects-toVitamin D
connects-toOmega 3 Fatty Acids
connects-toLeptin
connects-toPd 1
connects-toAdiponectin
connects-toResistin
connects-toOligodendrocyte
connects-toSystemic Lupus Erythematosus
connects-toSystemic Sclerosis
connects-toIl 12
connects-toIge
connects-toMast Cell
connects-toIl 31
connects-toT Cytotoxic Cell
connects-toFactor H
connects-toTslp
connects-toSelenium
connects-toC1 Esterase Inhibitor
connects-toOsteopontin
connects-toTransferrin
connects-toBradykinin
connects-toErythropoietin
connects-toHistamine
connects-toPeriostin
connects-toMelatonin
connects-toProlactin
connects-toTestosterone
connects-toSerotonin
connects-toOxytocin
connects-toVasopressin
connects-toIodine
connects-toCopper
connects-toZinc
connects-toPhosphorus
connects-toIron
connects-toChloride
connects-toNitrogen
connects-toCarbon
connects-toHydrogen
connects-toOxygen
connects-toSulfur
connects-toGlp 1
connects-toAngiotensin Ii
connects-toWnt Beta Catenin
connects-toRankl
connects-toSmad4
connects-toFibronectin
connects-toNotch
connects-toIgf 1
connects-toActivin A
connects-toCalcitonin
connects-toCgrp
connects-toSubstance P
connects-toInsulin Receptor
connects-toAldosterone
connects-toAndrogen Receptor
connects-toNorepinephrine
connects-toAdrenomedullin
connects-toFgfr
connects-toEpinephrine
connects-toRenin
Sources
- Wingerchuk DM, Banwell B, Bennett JL, et al. International consensus diagnostic criteria for neuromyelitis optica spectrum disorders. Neurology. 2015;85(2):177-189. · PubMed 26092914
- Pittock SJ, Berthele A, Fujihara K, et al. Eculizumab in Aquaporin-4-Positive Neuromyelitis Optica Spectrum Disorder. N Engl J Med. 2019;381(7):614-625. · PubMed 31050279
- Cree BAC, Bennett JL, Kim HJ, et al. Inebilizumab for the treatment of neuromyelitis optica spectrum disorder (N-MOmentum). Lancet. 2019;394(10206):1352-1363. · PubMed 31495497
- Yamamura T, Kleiter I, Fujihara K, et al. Trial of Satralizumab in Neuromyelitis Optica Spectrum Disorder. N Engl J Med. 2019;381(22):2114-2124. · PubMed 31774951