Atlas One · Host Biology · Scale 07 — System

Pemphigus Vulgaris

Pemphigus vulgaris (PV) is an IgG4-mediated autoimmune blistering disease targeting Dsg3 (mucous membranes) and Dsg1 (skin); suprabasal acantholysis. Rituximab (PEMPHIX: 90% vs 28% CR; FDA Jun 2018) and efgartigimod (ADHERE-SC; FDA Oct 2023) are approved therapies.

Also known as: pemphigus vulgaris, PV, pemphigus, pemphigus foliaceus, PF, autoimmune blistering disease, AIBD, anti-Dsg3, intraepidermal pemphigus

Scale 07 — SystemScale
draftStatus
2026-06-07Last Reviewed
This is an auto-generated stub page built from atlas entry frontmatter. A richer hand-crafted page is planned. See the atlas source for the full entry including detailed body sections.
pemphigus-vulgaris

Pemphigus Vulgaris

Pemphigus vulgaris (PV) is an IgG4-mediated autoimmune blistering disease targeting Dsg3 (mucous membranes) and Dsg1 (skin); suprabasal acantholysis. Rituximab (PEMPHIX: 90% vs 28% CR; FDA Jun 2018) and efgartigimod (ADHERE-SC; FDA Oct 2023) are approved therapies.

Entry Metadata

FieldValue
IDpemphigus-vulgaris
NamePemphigus Vulgaris
Statusdraft
Last reviewed2026-06-07
Atlas01-human
Scale07-system

Cross-Atlas Connections

connects-toDesmoglein 3 connects-toImmunoglobulin G connects-toCd20 connects-toFcrn connects-toB Cell connects-toEgfr connects-toComplement C3 connects-toSkin connects-toPlasma Cell connects-toT Helper Cell connects-toMyasthenia Gravis connects-toSystemic Lupus Erythematosus connects-toDermatomyositis connects-toRegulatory T Cell connects-toRheumatoid Arthritis connects-toType 1 Diabetes connects-toDendritic Cell connects-toIl 4 connects-toEye connects-toImmune System connects-toIntegumentary System connects-toDigestive System connects-toMhc Class Ii connects-toComplement C5 connects-toIl 6 connects-toCalcium connects-toCortisol connects-toMast Cell connects-toNf Kb connects-toIl 17A connects-toT Cytotoxic Cell connects-toSodium connects-toThymus connects-toNeutrophil connects-toElectron connects-toPhoton connects-toAcetylcholine connects-toCollagen connects-toOsteoporosis connects-toLung connects-toAntibody connects-toStaphylococcus Aureus connects-toReproductive System connects-toBaff connects-toCll connects-toVitamin D connects-toBtk connects-toSepsis connects-toThyroid connects-toTnf Alpha connects-toSjogrens Syndrome connects-toVenous Thromboembolism connects-toStat3 connects-toPneumocystis Jirovecii connects-toCandida Albicans connects-toType 2 Diabetes connects-toAspergillus Fumigatus connects-toMajor Depressive Disorder connects-toVaricella Zoster Virus connects-toHepatitis B Virus connects-toGeneralized Anxiety Disorder connects-toWound Healing connects-toEndocrine System connects-toMusculoskeletal System connects-toRespiratory System connects-toCardiovascular System connects-toLymphatic System connects-toCorticosteroids connects-toRenal System connects-toHerpesvirus connects-toCancer Chemotherapy connects-toCidp connects-toNmo connects-toGerminal Center connects-toPsoriasis connects-toSystemic Sclerosis connects-toIntestinal Epithelium connects-toAlveolus connects-toFollicular Lymphoma connects-toWaldenstrom Macroglobulinemia connects-toAnca Vasculitis connects-toCovid 19 Disease connects-toCdh1 connects-toIfn Gamma connects-toIl 1B connects-toIl 10 connects-toNlrp3 Inflammasome connects-toMacrophage connects-toSrc Kinase connects-toCaspase 3 connects-toCtla 4 connects-toJak1 2 connects-toIl 2 connects-toBcl 2 connects-toIl 13 connects-toTgf Beta connects-toIl 23 connects-toErk1 2 connects-toAkt connects-toIl 5 connects-toIl 12 connects-toMyd88 connects-toPik3Ca connects-toMtor connects-toGalectin 3 connects-toSmad4 connects-toStat1 connects-toCgas Sting connects-toFoxo connects-toS100A8 A9 connects-toGsk 3B connects-toPerforin connects-toAutophagy connects-toDnmt3A connects-toCcl2 connects-toAmpk connects-toCcr5 connects-toCalcineurin connects-toCxcl12 connects-toIl 33 connects-toType I Interferon connects-toGlucocorticoid Receptor connects-toIge connects-toThyroid Hormones connects-toSecretory Iga connects-toMu Opioid Receptor connects-toEstrogen connects-toNitric Oxide connects-toVegf connects-toXanthine Oxidase connects-toProstaglandins connects-toHistamine connects-toZinc connects-toIron connects-toPotassium connects-toMagnesium connects-toLeptin connects-toAdiponectin connects-toResistin connects-toNatural Killer Cell connects-toIl 31 connects-toTslp connects-toAtopic Dermatitis connects-toPrurigo Nodularis connects-toPeriostin connects-toC5Ar1 connects-toSelenium connects-toSubstance P connects-toFactor H connects-toC1 Esterase Inhibitor connects-toTransferrin connects-toBradykinin connects-toErythropoietin connects-toProlactin connects-toMelatonin connects-toOxytocin connects-toTestosterone connects-toSerotonin connects-toVasopressin connects-toCalcium connects-toIodine connects-toCopper connects-toPhosphorus connects-toChloride connects-toSulfur connects-toNitrogen connects-toOxygen connects-toCarbon connects-toHydrogen connects-toPd 1 connects-toGlp 1 connects-toAngiotensin Ii connects-toRankl connects-toWnt Beta Catenin connects-toFibronectin connects-toSmad4 connects-toIl 2 connects-toNotch connects-toIgf 1 connects-toActivin A connects-toCgrp connects-toCalcitonin connects-toInsulin Receptor connects-toAldosterone connects-toAndrogen Receptor connects-toNorepinephrine connects-toAdrenomedullin connects-toBdnf connects-toOsteopontin connects-toFgfr connects-toEpinephrine connects-toRenin connects-toMyostatin