Atlas One · Host Biology · Scale 07 — System

Dermatomyositis

Dermatomyositis is an immune-mediated myopathy with pathognomonic skin findings (heliotrope, Gottron's); type I IFN signature is central; MSAs (anti-MDA5, anti-TIF1γ, anti-NXP2, anti-Jo-1) stratify subtypes; IVIG (FDA Oct 2021), JAK inhibitors (baricitinib) are treatments.

Also known as: dermatomyositis, DM, idiopathic inflammatory myopathy, IIM, anti-MDA5 myopathy, amyopathic dermatomyositis, antisynthetase syndrome, juvenile dermatomyositis, JDM

Scale 07 — SystemScale
draftStatus
2026-06-07Last Reviewed
This is an auto-generated stub page built from atlas entry frontmatter. A richer hand-crafted page is planned. See the atlas source for the full entry including detailed body sections.
dermatomyositis

Dermatomyositis

Dermatomyositis is an immune-mediated myopathy with pathognomonic skin findings (heliotrope, Gottron's); type I IFN signature is central; MSAs (anti-MDA5, anti-TIF1γ, anti-NXP2, anti-Jo-1) stratify subtypes; IVIG (FDA Oct 2021), JAK inhibitors (baricitinib) are treatments.

Entry Metadata

FieldValue
IDdermatomyositis
NameDermatomyositis
Statusdraft
Last reviewed2026-06-07
Atlas01-human
Scale07-system

Cross-Atlas Connections

connects-toType I Interferon modulated-byImmunoglobulin G connects-toJak1 2 connects-toSkin connects-toCalcineurin connects-toLung connects-toEndothelial Cell connects-toSystemic Lupus Erythematosus connects-toMusculoskeletal System connects-toOvarian Cancer connects-toMacrophage connects-toSystemic Sclerosis connects-toNsclc connects-toPemphigus Vulgaris connects-toComplement C5 connects-toGastric Cancer connects-toT Helper Cell connects-toB Cell connects-toBreast Cancer connects-toHeart Failure connects-toDigestive System connects-toColorectal Cancer connects-toDendritic Cell connects-toCalcium connects-toCardiomyocyte connects-toT Cytotoxic Cell connects-toComplement C3 connects-toCortisol connects-toFibrosis connects-toOxygen connects-toLarge Intestine connects-toNf Kb connects-toPhoton connects-toPhosphorus connects-toHeart connects-toElectron connects-toKidney connects-toEye connects-toAntibody connects-toVegf connects-toPancreatic Cancer connects-toReproductive System connects-toStomach connects-toVitamin D connects-toStat1 connects-toVenous Thromboembolism connects-toPlasma Cell connects-toIl 6 connects-toRegulatory T Cell connects-toSjogrens Syndrome connects-toStat3 connects-toSepsis connects-toPneumocystis Jirovecii connects-toOsteoporosis connects-toCkd connects-toAnemia Of Chronic Disease connects-toPulmonary Arterial Hypertension connects-toAspergillus Fumigatus connects-toMajor Depressive Disorder connects-toIntegumentary System connects-toRespiratory System connects-toGeneralized Anxiety Disorder connects-toImmune System connects-toEndocrine System connects-toRenal System connects-toCardiovascular System connects-toLymphatic System connects-toNervous System connects-toCorticosteroids connects-toTargeted Therapy connects-toHerpesvirus connects-toCancer Chemotherapy connects-toMyasthenia Gravis connects-toCortical Bone connects-toAlveolus connects-toMyocardium connects-toAnca Vasculitis connects-toArterial Wall connects-toHnscc connects-toCheckpoint Inhibitors connects-toCovid 19 Disease connects-toEndometrial Cancer connects-toNeuromuscular Junction connects-toMhc Class Ii connects-toIfn Gamma connects-toIl 1B connects-toTnf Alpha connects-toIl 17A connects-toNlrp3 Inflammasome connects-toCd20 connects-toFcrn connects-toCcl2 connects-toRig I connects-toBaff connects-toEndothelin 1 connects-toMavs connects-toCgas Sting connects-toPd 1 connects-toC5Ar1 connects-toMyc connects-toIl 10 connects-toIl 12 connects-toIl 23 connects-toMyd88 connects-toGalectin 3 connects-toSmad4 connects-toErk1 2 connects-toS100A8 A9 connects-toHif 1Alpha connects-toFoxo connects-toAkt connects-toMtor connects-toGsk 3B connects-toPik3Ca connects-toPerforin connects-toSrc Kinase connects-toAmpk connects-toAutophagy connects-toCcr5 connects-toCxcl12 connects-toDnmt3A connects-toIl 33 connects-toTroponin Complex connects-toTgf Beta connects-toNitric Oxide connects-toIl 2 connects-toEstrogen connects-toIl 4 connects-toXanthine Oxidase connects-toProstaglandins connects-toIl 13 connects-toAngiopoietin connects-toHepcidin connects-toIron connects-toVon Willebrand Factor connects-toNsclc connects-toGastric Cancer connects-toLeptin connects-toAdiponectin connects-toResistin connects-toNatural Killer Cell connects-toRheumatoid Arthritis connects-toIl 5 connects-toMast Cell connects-toNeutrophil connects-toIge connects-toFibroblast connects-toTslp connects-toPeriostin connects-toFactor H connects-toC1 Esterase Inhibitor connects-toTransferrin connects-toBradykinin connects-toErythropoietin connects-toHistamine connects-toMelatonin connects-toProlactin connects-toOxytocin connects-toTestosterone connects-toSerotonin connects-toVasopressin connects-toSelenium connects-toIodine connects-toSodium connects-toMagnesium connects-toZinc connects-toCopper connects-toPotassium connects-toChloride connects-toSulfur connects-toNitrogen connects-toCarbon connects-toHydrogen connects-toGlp 1 connects-toAngiotensin Ii connects-toWnt Beta Catenin connects-toRankl connects-toFibronectin connects-toNotch connects-toIgf 1 connects-toActivin A connects-toCgrp connects-toCalcitonin connects-toSubstance P connects-toInsulin Receptor connects-toAldosterone connects-toAndrogen Receptor connects-toNorepinephrine connects-toAdrenomedullin connects-toBdnf connects-toOsteopontin connects-toFgfr connects-toEpinephrine