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dermatomyositis
Dermatomyositis
Dermatomyositis is an immune-mediated myopathy with pathognomonic skin findings (heliotrope, Gottron's); type I IFN signature is central; MSAs (anti-MDA5, anti-TIF1γ, anti-NXP2, anti-Jo-1) stratify subtypes; IVIG (FDA Oct 2021), JAK inhibitors (baricitinib) are treatments.
Entry Metadata
| Field | Value |
|---|---|
| ID | dermatomyositis |
| Name | Dermatomyositis |
| Status | draft |
| Last reviewed | 2026-06-07 |
| Atlas | 01-human |
| Scale | 07-system |
Cross-Atlas Connections
connects-toType I Interferon
modulated-byImmunoglobulin G
connects-toJak1 2
connects-toSkin
connects-toCalcineurin
connects-toLung
connects-toEndothelial Cell
connects-toSystemic Lupus Erythematosus
connects-toMusculoskeletal System
connects-toOvarian Cancer
connects-toMacrophage
connects-toSystemic Sclerosis
connects-toNsclc
connects-toPemphigus Vulgaris
connects-toComplement C5
connects-toGastric Cancer
connects-toT Helper Cell
connects-toB Cell
connects-toBreast Cancer
connects-toHeart Failure
connects-toDigestive System
connects-toColorectal Cancer
connects-toDendritic Cell
connects-toCalcium
connects-toCardiomyocyte
connects-toT Cytotoxic Cell
connects-toComplement C3
connects-toCortisol
connects-toFibrosis
connects-toOxygen
connects-toLarge Intestine
connects-toNf Kb
connects-toPhoton
connects-toPhosphorus
connects-toHeart
connects-toElectron
connects-toKidney
connects-toEye
connects-toAntibody
connects-toVegf
connects-toPancreatic Cancer
connects-toReproductive System
connects-toStomach
connects-toVitamin D
connects-toStat1
connects-toVenous Thromboembolism
connects-toPlasma Cell
connects-toIl 6
connects-toRegulatory T Cell
connects-toSjogrens Syndrome
connects-toStat3
connects-toSepsis
connects-toPneumocystis Jirovecii
connects-toOsteoporosis
connects-toCkd
connects-toAnemia Of Chronic Disease
connects-toPulmonary Arterial Hypertension
connects-toAspergillus Fumigatus
connects-toMajor Depressive Disorder
connects-toIntegumentary System
connects-toRespiratory System
connects-toGeneralized Anxiety Disorder
connects-toImmune System
connects-toEndocrine System
connects-toRenal System
connects-toCardiovascular System
connects-toLymphatic System
connects-toNervous System
connects-toCorticosteroids
connects-toTargeted Therapy
connects-toHerpesvirus
connects-toCancer Chemotherapy
connects-toMyasthenia Gravis
connects-toCortical Bone
connects-toAlveolus
connects-toMyocardium
connects-toAnca Vasculitis
connects-toArterial Wall
connects-toHnscc
connects-toCheckpoint Inhibitors
connects-toCovid 19 Disease
connects-toEndometrial Cancer
connects-toNeuromuscular Junction
connects-toMhc Class Ii
connects-toIfn Gamma
connects-toIl 1B
connects-toTnf Alpha
connects-toIl 17A
connects-toNlrp3 Inflammasome
connects-toCd20
connects-toFcrn
connects-toCcl2
connects-toRig I
connects-toBaff
connects-toEndothelin 1
connects-toMavs
connects-toCgas Sting
connects-toPd 1
connects-toC5Ar1
connects-toMyc
connects-toIl 10
connects-toIl 12
connects-toIl 23
connects-toMyd88
connects-toGalectin 3
connects-toSmad4
connects-toErk1 2
connects-toS100A8 A9
connects-toHif 1Alpha
connects-toFoxo
connects-toAkt
connects-toMtor
connects-toGsk 3B
connects-toPik3Ca
connects-toPerforin
connects-toSrc Kinase
connects-toAmpk
connects-toAutophagy
connects-toCcr5
connects-toCxcl12
connects-toDnmt3A
connects-toIl 33
connects-toTroponin Complex
connects-toTgf Beta
connects-toNitric Oxide
connects-toIl 2
connects-toEstrogen
connects-toIl 4
connects-toXanthine Oxidase
connects-toProstaglandins
connects-toIl 13
connects-toAngiopoietin
connects-toHepcidin
connects-toIron
connects-toVon Willebrand Factor
connects-toNsclc
connects-toGastric Cancer
connects-toLeptin
connects-toAdiponectin
connects-toResistin
connects-toNatural Killer Cell
connects-toRheumatoid Arthritis
connects-toIl 5
connects-toMast Cell
connects-toNeutrophil
connects-toIge
connects-toFibroblast
connects-toTslp
connects-toPeriostin
connects-toFactor H
connects-toC1 Esterase Inhibitor
connects-toTransferrin
connects-toBradykinin
connects-toErythropoietin
connects-toHistamine
connects-toMelatonin
connects-toProlactin
connects-toOxytocin
connects-toTestosterone
connects-toSerotonin
connects-toVasopressin
connects-toSelenium
connects-toIodine
connects-toSodium
connects-toMagnesium
connects-toZinc
connects-toCopper
connects-toPotassium
connects-toChloride
connects-toSulfur
connects-toNitrogen
connects-toCarbon
connects-toHydrogen
connects-toGlp 1
connects-toAngiotensin Ii
connects-toWnt Beta Catenin
connects-toRankl
connects-toFibronectin
connects-toNotch
connects-toIgf 1
connects-toActivin A
connects-toCgrp
connects-toCalcitonin
connects-toSubstance P
connects-toInsulin Receptor
connects-toAldosterone
connects-toAndrogen Receptor
connects-toNorepinephrine
connects-toAdrenomedullin
connects-toBdnf
connects-toOsteopontin
connects-toFgfr
connects-toEpinephrine
Sources
- Lundberg IE, Tjärnlund A, Bottai M, et al. 2017 European League Against Rheumatism/American College of Rheumatology classification criteria for adult and juvenile idiopathic inflammatory myopathies and their major subgroups. Arthritis Rheumatol. 2017;69(12):2271-2282. · PubMed 29106061
- Aggarwal R, Charles-Schoeman C, Schessl J, et al. Trial of Intravenous Immune Globulin in Dermatomyositis. N Engl J Med. 2022;387(14):1264-1278. · PubMed 36198072
- Sato S, Kuwana M. Clinicopathological features of Japanese patients with anti-CADM-140/MDA5 antibody-positive dermatomyositis. Arthritis Rheum. 2009;61(5):611-620. · PubMed 19405014
- Bohan A, Peter JB. Polymyositis and dermatomyositis. N Engl J Med. 1975;292(7):344-347. · PubMed 1090839